Goldenhar syndrome is a rare congenital defect involving first and second branchial arches and is characterized by incomplete development of nose, ear, palate, eyes, mandible and lip. It is also known as oculo-auriculo-vertebral syndrome. Reconstructive surgery is done to correct the facial defects and other structural abnormalities.

Keywords: Brachial arch, Ear tags, Goldenhar syndrome, Hypoplasia, Oculo-auriculo-vertebral syndrome.

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Dr Shiwani Thakur

Senior Resident, Department of Pediatrics, JLNMCH Bhagalpur, Bihar, India