Title: A case of non-immune hydrops fetalis with cystic hygroma complicated by intrauterine fetal death
Authors: Ayoub KHTIRA, Othmane ECHARFAOUI, Nassima OUGUERZI, Lina OUTIRIGHET, Intissar EL HALLAM, Moulay El Mehdi EL HASSANI, Jaouad KOUACH
DOI: https://dx.doi.org/10.18535/jmscr/v11i8.10
Abstract
Hydrops fetalis refers to the excessive accumulation of fluid in the extracellular compartment of the fetus. Cystic hygroma is a congenital malformation of the cervical lymphatic system responsible for an accumulation of lymphatic fluid commonly in the retrocervical region. Cystic hygromas are most often associated with chromosomal abnormalities. When a cystic hygroma is diagnosed in utero, the fetal survival rate is only 2-6%. When hydrops fetalis is present with cystic hygroma, the mortality rate is close to 100%. We present here the case of a 23-year-old primigravida in whom an ultrasound performed at 17 weeks of amenorrhea revealed a posterior cervical cystic hygroma associated with hydrops fetalis, the evolution of which was marked by intrauterine fetal death two weeks later.
Keywords: Hydrops fetalis, Cystic hygroma, Chromosomal abnormalities, Prenatal diagnosis.
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