Congenital cervical agenesis is a very uncommon condition. It usually coexists with congenital vaginal agenesis. Years back, many centers considered hysterectomy as the only treatment option. With the advent of newer techniques in reconstruction, most of these cases have achieved normal menstruation and few have had normal pregnancy as well. Herewith, we describe our experience in the management of primary amenorrhea in a 16 years old girl along with highlighting the unconventional uterovaginal anastomosis with V-M technique and thereby, we were able to achieve a successful outcome.

Keywords: Cervical agenesis/dysgenesis, congenital malformations, MRKH, obstructive Mullerian anomalies, vaginal agenesis.

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Dr Ramya R.S

MBBS, DGO, DNB (Dept of Obstetrics and Gynaecology)