Title: Radiation Therapy in Rosai Dorfman Disease Involving Long Bone- A Case Report
Authors: Dr Himanshi Jain, Dr Maitrik Mehta, Dr U. Suryanarayan, Dr Ankita Parikh, Dr Dinesh Anand, Dr Krishna Ratanchandani, Dr Nikhil Bathija, Dr Viraj Modi, Dr Siddharth Malukar, Dr Dhara Patel
DOI: https://dx.doi.org/10.18535/jmscr/v9i9.09
Abstract
Introduction
Rosai Dorfman disease, a rare, benign, proliferative, histiocytic disorder is also known as sinus histiocytosis with massive lymphadenopathy. Patients with this disease usually present with fever leukocytosis and painless cervical lymphadenopathy. It can also present at extra-nodal sites, commonly skin, soft tissue, central nervous system, and rarely bone.
There are no established treatment guidelines in this disease and there are very few reports discussing radiation therapy in Rosai Dorfman disease, although various modalities can be used for the treatment including surgery and chemotherapy also.
We present a case of 27 year old male patient with Rosai Dorfman disease of right knee treated at our institute and approach to its management. Patient is on monthly follow up since 6 months and is symptom free.
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