Hereditary spherocytosis (HS) is an autosomal dominant type of congenital haemolytic anaemia. The spherocytes are susceptible to osmotic lysis resulting in anaemia, jaundice, splenomegaly, cholelithiasis and altered the liver function. The management of hereditary spherocytosis is largely dependent on the severity of anaemia and degree of haemolysis. The anaesthetic management of a patient with HS and cholelithiasis for splenectomy and open cholecystectomy is discussed here.

Keywords: Hereditary Spherocytosis; Haemolysis; Splenomegaly; Splenectomy.

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Dr Arun B V

Final year postgraduate, Department of Anesthesiology, Chettinad Hospital and Research Institute