Title: Small Intestine Perforation as Initial Presentation of Granulomatosis with Polyangiitis
Authors: Firdevs ULUTAŞ, Tuğba AYTEKİN, Özgür ERAY, Veli ÇOBANKARA, Mevlüt ÇERİ, Uğur KARASU
DOI: https://dx.doi.org/10.18535/jmscr/v8i7.97
Abstract
Granulomatosis with polyangiitis (GPA) is necrotising vasculitis of small and medium sized blood vessels. GPA typically affects the upper/lower respiratory system and kidneys. Gastrointestinal system involvement is rarely seen. In the present paper, we report a case of small intestinal perforation as a presenting clinical manifestation in a patient with systemic GPA. The patient initially underwent surgical repair, and than achieved remission with methylprednisolone and cyclophosphamide.
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