Kawasaki disease is an acute, self-limited vasculitis of unknown aetiology that occurs predominantly in infants and children mostly below 5 years. It is considered the leading cause of acquired heart disease in children in developed countries. Diagnosis is mostly based on clinical features. Atypical Kawasaki diseases are patients who do not meet all the requisite criteria for diagnosis. Treatment includes high dose IVIG and aspirin. Most dreaded complication is coronary artery aneurysm (CAA). CAA occurs in 25-35 % 0f untreated cases and can occur in <5 % cases treated with IVIG. A second dose of IVIG is given if the patient does not improve. Over the last few years, several newer treatment option as second and third line have been explored.

Here we are going to report 3 cases of Kawasaki disease with varied presentation admitted to PIPD MKCG MCH, in the month of April i.e. peak of Covid 19 era.

Keywords: Kawasaki, vasculitis, IVIG, aspirin, coronary artery aneurysm.

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Dr Dibya Ranjan Panda

JR-2, Dept of Paediatrics, MKCG MCH, Berhampur, ODISHA