Title: Primitive Neuroectodermal Tumor in a Cirrhotic Liver: An Autopsy Finding
Authors: Sumiti Gupta MD, Priyanka Rawat, Shivani Malik MD, Nisha Marwah MD, Sunita Singh MD
DOI: https://dx.doi.org/10.18535/jmscr/v8i4.85
Abstract
Primitive neuroectodermal tumor is a rare neural crest tumor belonging to the Ewing’s sarcoma group of tumors. It constitutes approximately 1% of all sarcomas. Visceral involvement has been increasingly described in pancreas, vagina, stomach, small bowel, ovaries, oesophagus and kidney. However, primary visceral PNET are extremely rare, two cases of small intestine and hepatic duct involvement have been reported in children. It is a rare presentation in a visceral organ like liver. To the best of our knowledge only one or two cases of primitive neuroectodermal tumor of liver have been reported. It is a rare presentation in a visceral organ like liver. Here we present a case report of 56 year old deceased male whose viscera including heart, liver and kidneys were received for histopathological examination. The histopathological examined of liver revealed primary primitive neuroectodermal tumor along with cirrhosis.
Keywords: Primitive neuroectodermal tumor, Liver.
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