Title: Telescopic Nail in Osteogenesis Imperfecta Early Experience in Nitor
Authors: Dr R.A.M. Kausarul Islam, Dr Zahid Ahmed, Dr Malay Kumar Saha, Dr Ripon Kumar Roy, Dr Md. Mizanur Rahman, Dr Golam Faruque
DOI: https://dx.doi.org/10.18535/jmscr/v8i4.05
Abstract
Paediatic long bone lesions often need to be fixed or stabilized as a part of the treatment. But difficulties arise due to the bone is growing on. Osteogenesis Imperfecta is a genetic disorder that mainly affects the bone. It results in bones that break easily & deformed. It has no cure. The incidence ratio of OI is 1: 20000 to 1:50000 live births. For many years, Surgical Correction of deformities, physiotherapy and the use of orthotic support devices were the primary treatment. Intramedullary Fixation with the use of Telescopic Rod is one of the Standard Methods for long bone Stabilization in Growing children with Osteogenesis Imperfecta. Surgical Technique, Preoperative Radiographs are thoroughly evaluated to assess the deformity & to estimate the length and diameter of the Rods to be used. However, for severely angulated limb segments, we determined the Rod length intra-operatively, after performing multiple Osteotomies. From June 2016 to June 2018 in NITOR, we managed 9Tibiae 6 Femur by Telescopic Nail at the age of 2 to 12 years.
Keywords: Telescopic Nail, Osteogenesis Imperfecta, Surgical Technique, Preoperative Radiographs.
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