Congenital melanocytic nevus is usually defined as a melanocytic lesion which presents within 2 years of birth. Giant congenital melanocytic nevus (GCMN) has incidence of approximately <1:20,000 newborns. Despite being rare, GCMN is significant because of its association with severe complications such as malignant melanoma and neurocutaneous melanosis. GCMN presents as a brown lesion, with flat or mammilated surface, well-demarcated borders and hypertrichosis. Congenital melanocytic nevus is primarily a clinical diagnosis. Although GCMN is recognized as a risk factor for the development of melanoma, the precise magnitude of this risk is still controversial. The estimated lifetime risk of developing melanoma varies from 5 to 10%. On account of these uncertainties and the size of the lesions, the management of giant congenital melanocytic nevus needs individualization. Treatment may include surgical and non-surgical procedures, psychological intervention and/or clinical follow-up, with special attention to changes in color, texture or on the surface of the lesion. Indication for surgery in GCMN is the development of a malignant neoplasm on the lesion.

Keywords: Nevi; melanomas; Nevus, pigmented; Skin neoplasm.

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Dr Mohit Bajaj

Senior Resident, Department of Pediatrics DR RPGMC TANDA