Title: A rare case of Rosai-Dorfman disease with sellar, supra sellar involvement and bilateral cavernous sinus extension
Authors: Lokeshwar Reddy.C, Einstein Raju, Anand Rajamani, Sofia Bhansal
DOI: https://dx.doi.org/10.18535/jmscr/v8i3.78
Abstract
Rosai-Dorfman diasease or Sinus histiocytosis with massive lymphadenopathy (SHML) is a disease of unknown etiology. It is a rare non neoplastic histiocytic proliferative disorder that usually presents as bilateral massive lymphadenopathy in cervical regions of neck. It can also involve multiple various extranodal organ systems like eyes, skin, sinuses in less than 30% of cases. Bone involvement in associated with nodal disease are noted in less than 10% of cases. A Very few cases have been reported in literature with sellar or suprasellar involvement of Rosai-Dorfman disease. We report a very uncommon case of Rosai–Dorfman disease with sellar, supra sellar involvement and bilateral cavernous sinus extension
Keywords: Rosai–Dorfman disease, sella, supra sella, cavernous sinus.
Key message: sellar and supra sellar involvement with bilateral cavernous sinus extension is very rare.
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