Title: Recurrent Intestinal Obstruction with Multiple Intussusception in a Patient of Peutz-Jeghers Syndrome
Authors: Dr Naresh Kumar Damerla, Dr Thogari Kranthi Kumar
DOI: https://dx.doi.org/10.18535/jmscr/v7i7.08
Abstract
Peutz-jeghers syndrome (PJS) is a rare hamartomatous polyposis syndrome characterised by the presence of intestinal polyps and mucocutaneous melanotic pigmentataion. It is associated with various gastrointestinal and extraintestinal malignancies. This case report deals with the clinical presentation, investigations, operative findings, and outcome of a 10-year-old male child harboring this disease.
Keywords: intestinal obstruction, multiple intussusceptions, Intestinal hamartomatous polyps, Peutz–Jeghers syndrome.
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