Malignant round cell tumour includes a group of neoplasm characterized by cells that are small, round and relatively undifferentiated. MSRCT of PNS is relatively uncommon and presents with nasal discharge, polyp, mouth breathing, snoring, headache.

Detailed clinical history as well as radiological imaging specially CT is essential, the diagnosis is made by biopsy and IHC studies.

Treatment modalities include chemotherapy, radiotherapy or both are initiated as soon as the diagnosis is made, keeping in view the poor progression and aggressive nature of MSRCT.

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Dr V P Narve

Professor and Head, Department of ENT, Jaya Arogya Hospital, Gwalior, MP, India