Scimitar syndrome or pulmonary veno lobular syndrome is a rare complex cardio-pulmonary anamoly characterised by partial anamolous pulmonary venous connection. It can present as infant or adult form. We present a case of adult female evaluated for breathlessness had mild right heart dilatation and turned out to be adult form of scimitar syndrome, along with brief review of literature.

Keywords-Scimitar syndrome, Anamolous pulmonary venous connection, rare cuase of dyspnea.

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Dr Rohit Thakare

Department of Cardiology, Bombay Hospital Institute of Medical Sciences, Mumbai

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