Title: Dyke-Davidoff-Masson syndrome with Coarctation of Aorta: Case Report of A Novel Association
Authors: Dr Hargurdas Singh, Dr Prateek Mangal, Dr Dinesh Yadav, Dr Santosh Kumar
DOI: https://dx.doi.org/10.18535/jmscr/v7i1.149
Abstract
Introduction
Dyke-Davidoff-Masson syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere (hemiatrophy), which is usually due to an insult to the developing brain in fetal or early childhood period1.DDMS is described as skull radiographic and pneumatoencephalographic changes in their series of nine patients whose clinical characteristics included hemiparesis, seizures, facial asymmetry, and mental retardation which was proposed in 1933 by Dyke et al2.The clinical findings may be of variable degree according to the extent of the brain injury. The following is a case presentation of a young male who presented with complaints of recurrent seizures and subsequently diagnosed as having coarctation of aorta (CoA). Neuroimaging findings were suggestive of DDMS. The present case is still remaining an enigma to us and no previous documentation of hemicerebral atrophy in the context CoA has been found in the literature.
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