Vein of Galen malformations are rare anomalies that constitute only 1% of all intracranial malformations.

35 Year Old Female Presented with Deviation of angle of mouth to the right side associated with giddiness. MRI Brain with MRV done, Showed vein of galen malformation (median prosencephalic AV fistula) causing mass effect and obstructive hydrocephalus. Because of its rarity in adults, there is still insufficient information about this disease during adult age.

1. Vein of Galen malformations: Review A. K. Gupta, D. R. Varma Department of Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvendram
2. Gupta, DR. Varma "Vein of Galen malformations: Review" Neurology India March 2004 Vol 52 Issue 1journal of Perinatology (2005) 25, 542–551. doi:10.1038/sj.jp.7211349; published online 14 July 2008.
3. Diagnosis and Management of Vein of Galen Aneurysmal Malformations, Philippe Gailloud MD1, Declan P O'Riordan MD2, Ingrid Burger BS1, Olivier Levrier MD1,5, George Jallo MD3, Rafael J Tamargo MD4, Kieran J Murphy MD1 and Christoph.
4. U Lehmann MD2 Vein of Galen aneurysmal malformations: critical analysis of the literature with proposal of a new classification system A review Martin
5. Mortazavi, M.D.,1 Christoph J. Griessenauer, M.D.,1 Paul Foreman, M.D.,1 Reza Bavarsad Shahripour, M.D.,2 Mohammadali M. Shoja, M.D.,2 Curtis J. Rozzelle, M.D.,2 R. Shane Tubbs, Ph.D.,2 Winfield Stitt Fisher III, M.D.,1 and Takanori Fukushima, M.D.3 1
6. Division of Neurosurgery, Department of Surgery, University of Alabama at Birmingham; 2 Pediatric Neurosurgery, Children’s Hospital, Birmingham, Alabama; and 3 Division of Neurological Surgery, Dula University, Durham, North Carolina

Sowmiya .M

Final Year Postgraduate, Department of General Medicine