Acrogeria, Gottron type is a rare premature aging syndrome. Characteristic signs include fragile, thin skin on the hands and feet. Other parts of the body (e.g., face, forearms, and lower legs) are variably affected. It is generally considered to be a mild, non progressive skin atrophy due to the loss of the fatty tissue directly under the skin. Although most cases are sporadic, both autosomal recessive and autosomal dominant inheritance have been reported with a female predominance. Prognosis of these patients is good as they have no tendency to develop atheroma or diabetes mellitus. We report a case 11 year old female child of acrogeria for its rarity.

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Nasreen Ali

Junior Resident, Department of Pediatrics,

M.K.C.G Medical College, Berhampur, Ganjam, Odisha-760004, India