Title: Anorectal Malformations-An Experience from a Tertiary Referral Hospital
Authors: Samir Gupta MS,MCh (Paed Surgery), Shiju K Sreepathy, Achal Gupta
DOI: https://dx.doi.org/10.18535/jmscr/v6i3.54
Abstract
Objectives: This study was undertaken to find out various types anorectal malformations in local population, their sex distribution and compare that with available present day data, to study the incidence of various associated anomalies and to study the morbidity and mortality associated with it.
Study Design: 70 consecutive patients of anorectal malformation attending the Department of Surgery, Gajra Raja Medical College, Gwalior, India were included in the study. A detailed history was taken and thorough examination was performed for both the primary and associated anomalies. Necessary investigations were done. Management was done according to the protocol. The data was recorded and analyzed.
Results: Out of 70 patients 51 were males and 19 were females. Types of malformations were anorectal agenesis without fistula (17.14%), perineal membrane/fistula (15.71%), recto-vestibular fistula (11.43%), recto-urethral and recto-vescical fistulae (7.14% each) and rare anomalies like cloacal malformations (5.71%) and congenital pouch colon(8.57%). 49.01% of males and 15.79% females had associated anomalies. Urogenital system was involved in 15.72%, cardiovascular and skeletal systems in 10% each, respiratory system and gastrointestinal system in 7.14% each and nervous system in 4.29% of patients. There were 11 deaths and 6 of those had severe associated anomalies.
Conclusions: Anorectal malformations occurred commonly in males. High anomalies in males and intermediate anomalies in females were common. Commonest anomalies were rectovestibular fistula in females and anorectal agenesis without fistula in males. Urogenital anomalies were most commonly associated. Mortality was higher in males having high anomalies and in patients having severe associated anomalies.
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