Ewings sarcoma/Primitive Neuroectodermal tumors are a group of tumors characterised by small round cells seen in children and adolescence that rarely affect the bone and soft tissues of the nasal cavities. Incidence of tumors in head and neck is 2-7%^[1,2], with mandible and maxilla being the most common sites and sinonasal tract is very rare to involve^[1-3]. Here we report a case of Ewing’s sarcoma of nasal cavity in an 13 years old adolescent male who was diagnosed on histopathology at his local place as Esthesioneuroblastoma.

Keywords: Ewing’s sarcoma, Esthesioneuroblastoma, Peripheral neuroectodermal tumor, Sinonasal tract.

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Dr Lalitha Reddy.K.

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