Title: Angiomyolipoma of Kidney- A Case Report
Authors: Dr Gopinath Barui, Dr Tripti Das
DOI: https://dx.doi.org/10.18535/jmscr/v6i2.54
Abstract
Renal angiomyolipoma is an uncommon benign tumour characterized by a variable mixture of adipose tissue, smooth muscle and thickened blood vessels and hence the name. We here in, present a case of renal angiomyolipoma in a 60 years old female patient presenting with flank pain and swelling. Clinico-radiological evaluation suggested a mass lesion arising from kidney. Nephrectomy was carried out. The histological examination revealed admixture of spindle cells & adipose tissue along with thick walled blood vessels. The case was diagnosed as Angiomyolipoma of right kidney and the patient was followed up closely.
Keywords: renal angiomyolipomas, nephrectomy, PEComas ,mesenchymal, benign tumour.
References
- Folpe AL, Kwiatkowski DJ(2010). Perivascular epithelioid cell neoplasms:p athology and pathogenesis. Hum Pathol. 9:198-203.PMID:11981115; Martignoni G, Pea M, Reghellin D, Zamboni G,Bonetti F(2008). PEComas: the past, the present and the future.Virchows Arch.452:119-32.PMID:18080139 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Fujji Y, Ajima J,Oka K,Tosaka A, TakeharaY (1995) Benign renal tumours detected among healthy adults by abdominal ultrasonography. Eur Urol.27: 124-7.PMID:7744154 (WHO Classific-ation of Tumours of the Urinary System and Male Genital Organs,2016)
- Steiner MS, Goldman SM, Fishman EK, Marshall FF(1993).The natural history of renal angiomyolipoma. 150:1782-6.PMID: 8230504 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Cook JA,Oliver K, Mueller RF, Sampson J (1996). Across sectional study of renal involvement in tuberous sclerosis. J Med Genet.33:480-4.PMID:8782048 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Sternberg’s Diagnostic Surgical Pathology,6th Edition, Page no. 2003
- Morgan GS, Straumford JV and Hall E: Angiomyolipoma of the kidney.J Urol65:525-527,1951.
- Green AJ, Sepp T,Yates JR (1996). Clonality of tuberous sclerosis hamartomas shown by non-random X chromosome inactivation. Hum Genet.97:240-3.PMID:8566961 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Tallarigo C, Baldassarre R, Bianchi G, Comunale L, Olivo G,Pea M et al.(1992). Diagnostic and therapeutic problems in multicentric renal angiomyolipoma. J Urol.148:1880-4.PMID:1433628 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Steiner MS, Goldman SM, Fishman EK, Marshall FF (1993).The natural history of renal angiomyolipoma. 150:1782-6.PMID: 8230504 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016)
- Nese N, Martignoni G, Fletcher CD, Gupta R, Pan CC, Kim H, et al. Renal perivascular epithelioid cell tumors [(PEComa), so called epithelioidangio-myolipoma (EAML)]: analysis of61 cases including 44 withpure/predominant epithelioid (PPEComa) morphology and parametersassociated with malignant outcome. LabInvest 2009; 89 (Suppl 1):186A.
- Schillinger F,Montagnac R (1996).Chronic renal failure and its treatment in tuberous sclerosis. Nephrol Dial Transplant.11:481-5.PMID:8671819 (WHO Classification of Tumours of the Urinary System and Male Genital Organs,2016).
- Taylor Rs, Joseph DB, Koham EC, Wilson ER, Bueschen Al. Renal angiomyolipoma associated wall lymph node involvement and renal cell carcinoma in patients with tuberous sclerosis. l Urol 1989; 141: 930-2.
- Mikami S, Oya M, Mukai M. Angiomy-olipoma with epithelial cysts of the kidney in a man. Pathol Int. 2008 Oct; 58(10): 664-7.