Title: Rosai Dorfman Syndrome (Sinus Histiocytosis with Massive Lymphadenopathy)
Authors: Dr Jeyhan B. Dhabhar, Dr Jaishree Ghanekar
DOI: https://dx.doi.org/10.18535/jmscr/v5i11.88
Abstract
Sinus histiocytosis with massive lymphadenopathy (Rosai Dorfman disease) is an uncommon benign condition, often confused with lymphoma. Patients usually have massive enlargement of cervical lymph nodes. We describe here a 63 year old male patient who presented with generalised massive lymphadenopathy & tonsillar enlargement. His histopathology report was suggestive off Sinus histiocytosis with massive lymphadenopathy. He was started on low dose steroids and recovered completely.
Keywords: Lymph nodes, Rosai-Dorfman disease, sinus histiocytosis with massive lymphadenopathy (SHML)
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