Title: Congenital Heart Disease (Atrial Septal Defect) With Rheumatic Heart Disease (Mitral Regurgitation)-A Rare Association
Authors: Nasreen Ali, Sunil Kumar Agarwalla
DOI: https://dx.doi.org/10.18535/jmscr/v5i7.115
Abstract
Mitral regurgitation (MR) associated with secundum atrial septal defect could exist as an coexistent lesion or as the result of hemodynamic change occurred in secundum atrial septal defect. The etiologies are rheumatic valve, prolapsed anterior leaflet, congenital abnormality, specific pathology complex, and chronic infective endocarditis.
Here we report a case of 13 year old female child who was admitted to paediatric emergency department of MKCG medical college with complains of fast breathing and respiratory difficulty since last 7 days. On examination, there was paedal edema and murmur was heard at aortic and mitral area. On further investigations it was confirmed to be a case of Atrial septal defect (ASD) with Rheumatic heart disease (RHD).
Like in Lutembacher syndrome a combination of congenital ASD and acquired almost always rheumatic mitral stenosis, we propose that this combination of congenital ASD with MR due to rheumatic origin should be recognized with a name.
Keywords: rheumatic valve, prolapsed anterior leaflet, congenital abnormality, specific pathology complex, chronic infective endocarditis.
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