Title: Sickle Cell Nephropathy Presenting as Type 4 Renal Tubular Acidosis and Hyperkalemia
Authors: Jahnabi Bhagawati, Sourya Acharya, Samarth Shukla, Abhijeet K. Agrawal
DOI: https://dx.doi.org/10.18535/jmscr/v5i6.134
Abstract
Sickle cell nephropathy (SCN) is a well known clinical entity. Various pathophysiological mechanisms and risk factors alter the renal functions in sickle cell disease (SCD). The renal manifestations ranges from glomerular insults, vasculopathy, tubular dysfunctions and even malignancies like renal medullary carcinoma. We present a case of a 20 year male who presented to us with sickle cell crisis and severe hyperkalemia due to rare type 4 distal renal tubular acidosis (RTA).
Key Words: SCN, SCD, vasculopathy, glomerular, hyperkalemia, RTA.
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