Title: A Rare Cause of Congenital Bronchiectasis – Mounier Kuhn Syndrome
Authors: Dr T.Bindu.MBBS.MD, Dr A.D.Nageswari.MBBS.DTCD.MD, Dr H.Peer Mohaideen.MBBS
DOI: https://dx.doi.org/10.18535/jmscr/v5i6.61
Abstract
Tracheobronchomegaly also called ”Mounier Kuhn Syndrome" is a rare congenital disorder of the lung characterised by an abnormal widening of the trachea and main stem bronchi.lt is usually associated with recurrent lower respiratory tract infection, bronchiectasis and tracheal diverticulitis with or without respiratory complications The disease was first described in 1932 and since then, only few hundreds of cases have been reported. Symptoms usually appear in fourth to sixth decade of life and is usually similar to chronic bronchiectasis due to any other cause. Diagnosis depends on enlarged trachea and proximal bronchi on plain radiograph and CT-Chest. Treatment is mainly supportive. We report a case with this condition for its rarity.
Keywords: Mounier Kuhn, bronchiectasis, trachealdiverticulosis.
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