Title: Primary Ewing Sarcoma at Rare Sites – A Study of Few Cases
Authors: Guddi Rani Singh, Rawi Agrawal, Vijayanand Choudhary, Ajeet Kumar, Amit Kumar Sinha, Krishna Kumar Singh
DOI: https://dx.doi.org/10.18535/jmscr/v5i5.105
Abstract
The Ewing family of tumors includes classic Ewing Sarcoma (ES), atypical ES, primitive neuroectodermal tumor (PNET), and Askin tumor. It is a small round blue cell tumor involving most commonly the diaphyses of long bones. We present a series of four cases of ES occurring at rare sites.
Keywords: Ewing’s sarcoma, PNET, small round cells, FLI-1, CD99.
References
1. Desai KI, Nadkarni TD, Goel A, Muzumdar DP, Naresh KN, Nair CN. Primary Ewing's sarcoma of the cranium. Neurosurgery. 2000;46:62-68.
2. Sim FH, Unni KK, Beabout JW, Dahlin DC. Osteosarcoma with small cells simulating Ewing's tumour. Bone and Joint Surg. 1979;61:207-15.
3. Karatziou C, Pitta X, Stergiouda T, Karadimou V, Termentzis G. A case of extraskeletal Ewing sarcoma originating from the visceral pleura.Hippokratia 2011, 15, 4: 363-365.
4. van den Berg H, van Rijn RR , Merks JH. Management of Tumors of the Chest Wall in Childhood: A Review. J Pediatr Hematol Oncol 2008;30:214-221.
5. Iwamoto Y. Diagnosis and Treatment of Ewiing’s Sarcoma. Jpn J ClinOncol 2007;37:79-89.
6. Sim FH, Unni KK, Beabout JW, Dahlin DC. Osteosarcoma with small cells simulating Ewing's tumour. Bone and Joint Surg. 1979;61:207-15.
7. Singh P, Jain M, Singh DP, Kalra N, Khandelwal N, Suri S. MR findings of primary Ewing’s sarcoma of greater wing of sphenoid. Australas Radiology. 2002;46:409- 11.
8. Pollard SG, Marks PV, Temple LN, Thompson HH. Breastsarcoma. Aclinicopathologic review of 25 cases. Cancer 1990;66:941-4.
9. Vindal A, KakarAK..Primary primitive neuroectodermal tumor of the breast. J Clin Oncol2010;28:e453-5
10. Peersman B, Vanhoenacker FM, Heyman S, et al. Ewing’s sarcoma: imaging features. JBR–BTR. 2007; 90(5):368–376.
11. Reinus WR, Gilula LA. IESS Committee: radiology of Ewing’s sarcoma: intergroup Ewing’s sarcoma study. Radiographics. 1984; 4:929–944.
12. Ozge C, Calikoglu M, Cinel L, Apaydin FD, OzgurES.Massive pleural effusion in an 18-year-old girl with Ewing sarcoma. Can Respir J 2004 Jul- Aug;11(5):363-365.
13. Wolf G, Aigner RM, Schwarz T. Massive pleural effusion with dyspnea in a 17-year-old boy as the first sign of ewing sarcoma. J Pediatr Hematol Oncol 2002 Jun-Jul;24(5):420.
14. Ozge C, Calikoglu M, Cinel L, Apaydin FD, OzgurES. Massive pleural effusion in an 18-year-old girl with Ewing sarcoma. Can Respir J 2004 Jul- Aug;11(5):363-365
15. Lee WS, Kim YH, Chee HK, Hwang JJ, Kim JS, Lee SA, et al. Multimodal Treatment of Primary Extraskeletal Ewing’s Sarcoma of the Chest Wall: Report of 2 Cases. Cancer Res Treat.2009; 41: 108–112.