Title: Limited Wegener’s Granulomatosis Associated with Multiple Pyoderma Gangrenosum Lesions in a 30 Year Old Indian Woman
Authors: Dr Pragya Gupta, Dr Mudita Gupta, Dr Shikha Sharma, Dr GR Tegta
DOI: https://dx.doi.org/10.18535/jmscr/v5i2.81
Abstract
Pyoderma gangrenosm is a neutrophilic dermatosis characterised by rapidly spreading and painful ulceratve lesions. Wegener’s granulomatosus, a small vessel vasculitis can present with cutaneous features in approximaely 10% of patients. There can be subcutaneous nodules, papulonecrotic lesions, ulcers which may resemble pyoderma gangrenosum so called ‘malignant pyoderma’. We hereby report a rare case of 30 year old female with multiple pyoderma gangrenosum lesions associated with upper respiratory tract, ear, sinus involvement with positive p-ANCA subsequently diagnosed as limited wegener’sgranulomatosus with pyoderma gangrenosum. Patient was treated with steroids and immunosuppressives showed significant improvement over time.
Keywords: Pyoderma Gangrenosum, Wegeners granulomatosis , pANCA.
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