Title: Colonic Adenocarcinoma Presenting as Hemophagocytic Syndrome: A Case Report
Authors: Murtaza Ali, Birakta Debbarma, Arvind Kumar
DOI: https://dx.doi.org/10.18535/jmscr/v5i2.56
Abstract
Hemophagocytic syndrome is a rare and potentially fatal disorder characterised by pathological immune activation associated with primary familial disorder, genetic mutation or occurring as a sporadic condition. The later can be secondary to infections, malignancies or autoimmune diseases. Malignancy associated HLH is commonly seen in haematological malignancies and rarely with solid organ tumours.
We report a case of "Adenocarcinoma of colon" presenting as Hemophagocytic syndrome, to our knowledge, this is the first case report of HLH secondary to Carcinoma colon, a rare presentation of solid organ malignancy.
Keywords: Hemophagocytosis, Carcinoma colon, Malignancy.
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