Title: A Rare Case of Retroperitoneal Lymphatic Cyst in Adult
Authors: Dr A.K Nayak, Dr P Hembram, Dr A. Pradhan, Dr D.K Jha, Dr M Nayak
DOI: https://dx.doi.org/10.18535/jmscr/v5i1.136
Abstract
Retroperitoneal lymphangioma is a rare, benign mesodermal tumor arising from the retroperitoneal lymphatics which usually presents in infancy and it is worthy to report a case when it has presented in an adult. Apart from being a rare entity it also presents as a diagnostic dilemma and final diagnosis is often made on surgical exploration. We report a case of retroperitoneal lymphangioma in a 58-year-old female who presented with abdominal distension and dull aching abdominal pain with loss of appetite. Radiological imaging revealed large globular cystic lesion of size 175mm x 160mm x115mm having well defined margin in the right side of abdominal cavity extending from subhepatic area to the right iliac region. It appears separate from the right kidney, liver and major vessels. Surgical removal of the cyst was accomplished without any incident. A benign cystic retroperitoneal lymphangioma was diagnosed on histology and confirmed with immunohistochemical stains.
Keywords: Retroperitoneum, Cystic, Lymphangioma.
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