Title: Primary Malignant Melanoma of Jejunum with Perforation Peritonitis: A Case Report
Authors: Vivek Vasudeo, Madhu Smita, Nishant, Shital Malua
DOI: https://dx.doi.org/10.18535/jmscr/v5i1.108
Abstract
Neuroendocrine tumours (NETs also known as carcinoid tumours), adenocarcinoma, GIST, lymphoma are the common malignant neoplasms of small bowel in that order. Malignant melanomas are the rare entities. They are found mostly as metastasis to small bowel. Primary malignant melanoma of small bowel is very rare with paucity of published reports. It can remain asymptomatic for long duration and is often diagnosed at an advanced stage or as in this case with perforation where no standardised management protocol is developed. The pathophysiology is debatable. It is currently challenging to differentiate primary and secondary gastrointestinal melanomas. In this case report, we have reported a case of primary malignant melanoma of jejunum presenting with perforation peritonitis. Laparotomyrevealed ablack, pigmented,ulceroproliferative jejunal massperoperatively. It was further confirmed on histopathology and immunohistochemistry as Malignant Melanoma. After ruling out the differentials and on retrograde specific clinical history and examination, the diagnosis of primary malignant melanoma of jejunum was made.
Keywords- primary malignant melanoma, jejunum, immunohistochemical, Gastrointestinal stromal tumour (GIST), metastasis, leiomyosarcomaand criteria.
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