Title: A 26 Year Old Male with Fever, Productive Cough, Hemoptysis and Epistaxis
Authors: M. Umar. Majid M.D DNB FCCP, C.P. Rauf M.D
DOI: http://dx.doi.org/10.18535/jmscr/v3i8.20
DIDS : 08.2015-XXXXXXXX
Abstract
We are presenting a case of Granulomatosis with polyangitis (GPA) formerly known as wegner’s granulomatosis in a young non smoker male who presented with fever, productive cough, hemoptysis, headache, and epistaxis of two months duration. He was earlier treated as a case of pulmonary tuberculosis with no significant improvement. On evaluation he was found to have paranasal sinus and lung involvement and his laboratory findings showed C ANCA (PR3) =102 u/ml, tissue biopsy from a polypoidal nasal mass showed granuloma with vasculitis, based on these findings he was diagnosed as a case of GPA and treated with Cyclophosphamide and Steroids with good response.
Keywords: GPA= Granulomatosis with polyangitis, C ANCA= cytoplasmic antineutrophil cytoplasmic antibodies
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