Title: Alveolar Rhabdomyosarcoma Arising From Maxillary Antrum in a Adult: A Rare Case Report
Authors: Amod Kumar, Anju Singh, Sanjeet Kumar Singh, M.A. Muzaffar, Subhash Chandra Jha, Shahab Raza, Rakesh Kumar Singh
DOI: http://dx.doi.org/10.18535/jmscr/v3i9.05
Abstract
Rhabdomyosarcoma is one of the most common soft-tissue sarcomas in children under 15 years of age, and the head and neck is the principal location for childhood rhabdomyosarcoma; however head and neck rhabdomyosarcoma is rare in adults, occasionally occurs in nasal cavity and paranasal sinuses, it is rare at this site in adults. The typical subtypes of embryonal, alveolar and pleomorphic rhabdomyosarcoma are diagnosed histopathologically. The markers connoting simple myogenous or skeletal muscle differentiation has contributed tremendously to the diagnosis of even poorly differentiated rhabdomyosarcoma .The alveolar variant is more commonly seen in extremities and is very unusual in nasal and paranasal sinuses. Desmin and myogenin were highly positive while others were negative. Thus, a rare diagnosis of alveolar rhabdomyosarcoma arising from maxillary antrum was confirmed. We present a rare case of Alveolar rhabdomyosarcoma at unusual site in an adult.
Keywords:Rhabdomyosarcoma, alveolar, adult, paranasal sinus
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