Title: Haemothorax in Thalassaemia May be a Complication of Rupture of Intrathoracic Extramedullary Haematopoiesis
Authors: Anirban Chatterjee, Suman Sarkar, Amrita Roy
DOI: http://dx.doi.org/10.18535/jmscr/v3i9.04
Abstract
Intrathoracic extramedullary hematopoiesis is reported in the literature but rare; typically found in the chronic hemolytic anemia. We report a beta-thalassaemia major patient, 11-y-girl, presented with hemothorax. Computed tomographic scan of the thorax showed many paravertebral and extra-pulmonary tumors. Biopsy revealed extramedullary haematopoiesis. Hemothorax in beta thalssemia should be suspicion about Intrathoracic extramedullary hematopoiesis because surgical intervention is first-line management.
Keywords: extramedullary haematopoiesis; haemothorax; thalassaemia
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