Introduction: A hemangiopericytoma is a rare soft tissue tumor of vascular origin representing 1% of all vascular neoplasms. It is derived from a pericyte of Zimmerman, which is a modified smooth muscle cell that surrounds the small blood vessels. Hemangiopericytoma can occur wherever there are vascular capillaries. In this paper, we report a case of hemangiopericytoma in retroperitoneal space.

Case Presentation: A 30-year-old male presented with a palpable lump on the left abdomen. Preoperative imaging indicated that the tumor was in the retroperitoneal space without invasion of other organs. A complete resection was performed via a midline incision. The histological and immunohistochemical staining patterns supported the diagnosis of a hemangiopericytoma.

Conclusion: Complete resection is the best way to treat a hemangiopericytoma. Despite its rare incidence in comparision with other mesenchymal tumors of retroperitoneal space, hemangiopericytoma should be considered in the differential diagnosis of well defined lobulated retroperitoneal masses.

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Dr Dreamy Jain

Junior Resident,

Department of Pathology, P.D.V.V.P.F's Medical College, Ahmednagar

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