Title: Neurofibroma Arising In the Parotid Gland- A Rare Case Report
Authors: Shagufta Qadri, Divya Rabindranath, Azka Anees Khan, Senthil P.
DOI: http://dx.doi.org/10.18535/jmscr/v4i1.15
Abstract
Neurofibromas of salivary gland are very rare and account for only 0.4% of all salivary gland neoplasms. Plexiform type of neurofibroma is predominantly seen in a scenario of neurofibromatosis 1 association, but solitary plexiform neurofibroma has also been occasionally reported. We present a report of this variant in a 17 year old male who presented with a slow growing painless swelling in the right pre auricular region for 8 months duration. Microscopic examination and immunostaining of the tumor confirmed the diagnosis of plexiform neurofibroma. We report this case in order to emphasize the importance of correctly recognizing this rare entity due to several reasons; including the difficulty in its complete excision, and a potential for malignant transformation in 10% cases. Therefore, correct diagnosis and a timely treatment with follow up are a necessity for this tumor.
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