Title: Takayasu Arteritis and PRES Syndrome - A Rare Case Series
Authors: Dr Ritu Gupta, Dr Sandeep Singh, Dr Tarunendra Kumar Mishra, Dr Ishan Verma
DOI: http://dx.doi.org/10.18535/jmscr/v4i1.12
Abstract
PRES is a very rare manifestation of Takayasu’s arteritis. It can present with headache, seizures, altered sensorium with visual disturbances. Two young teenager patients presented in ward with complaints of severe headache, Hypertention , vomiting ,blurring of vision followed by GTCS and altered sensorium for about one month.(1) Their routine investigations like CBC,LFT,RFT appears to be normal with raised ESR.CE-MRI of brain shows focal areas of hyperintensity scattered in white matter signs of PRES.CT angiography of abdominal aorta showed possibility of autoimmune vasculitis with bilateral proximal renal artery stenosis ,critical stenosis on right with small right kidney and decreased enhancement. Patients were put on antihypertensive and antiepileptic medication along with steroids to manage Takayasu’s Arteritis with PRES. These patient’s respond’s symptomatically and were referred to higher centre for recanalisation of renal artery stenosis.
Keywords - PRES-Posterior reversible encephalopathy syndrome, TA-Takayasu Arteritis, GTCS- Generalised Tonic Clonic seizures, CBC- Complete blood count, LFT- Liver fumction test, RFT-Renal function test.
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